Hydronephrosis caused by kidney malrotation

Urol Case Rep. 2021 Jan 11:36:101564. doi: 10.1016/j.eucr.2021.101564. eCollection 2021 May.

Abstract

Hydronephrosis associated with kidney malrotation can be a surgical challenge. We present the case of a 3.5 y.o.-boy presenting with left pyelo-ureteric obstruction caused by kidney hyperrotation (270°) resulting in recurring urinary tract infection. After complete radiological work-up, we opted for a primary laparoscopic ureterocalicostomy, which allowed for complete resolution of the pelvic dilatation. Kidney malrotation can present with a wide variation in anatomic features. Radiological work-up is the cornerstone of surgical strategy planning. Laparoscopic ureterocalicostomy is a useful primary option in unusual anatomical situations.

Keywords: Kidney malrotation; Laparoscopic ureterocalicostomy; Pediatric urology; Pyelo-ureteric joint obstruction.

Publication types

  • Case Reports