Radiation-induced sarcoma is a known but rare complication of radiation treatment for skull base paraganglioma. We present the cases of a female patient with multiple paraganglioma syndrome treated with external beam radiation treatment who presented 4 years later with a malignant peripheral nerve sheath tumor of the vagus nerve.
Keywords: glomus vagale; malignant peripheral nerve sheath tumor; paraganglioma; radiation; radiation-induced sarcoma; vagus nerve.
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