Recurrent Ulcerations in an 84-Year-Old Male Diagnosed with Hailey-Hailey Disease

Fahad Al Qooz; Mohammed Almuharraqi; Sajjad Salam; Veena Nagaraj; Abdullah Darwish

doi:10.1159/000510018

Recurrent Ulcerations in an 84-Year-Old Male Diagnosed with Hailey-Hailey Disease

Case Rep Dermatol. 2020 Nov 5;12(3):209-212. doi: 10.1159/000510018. eCollection 2020 Sep-Dec.

Authors

Fahad Al Qooz¹, Mohammed Almuharraqi¹, Sajjad Salam¹, Veena Nagaraj², Abdullah Darwish²

Affiliations

¹ Dental and Maxillofacial Department, Royal Medical Services, Riffa, Bahrain.
² Department of Pathology, Royal Medical Services, Riffa, Bahrain.

Abstract

Hailey-Hailey disease (HHD), or familial benign chronic pemphigus, is a rare inherited acantholytic dermatosis. It is an autosomal dominant disease affecting the intertriginous areas. HHD has been characterized by flaccid blisters, erosions, and macerations that are limited to flexural (friction-prone) areas. The painful blisters and erosions significantly decrease patients' quality of life. There are multiple types of therapy related to this disorder. Many of the studies have suggested benefits from steroid therapy in addition to oral antibiotics.

Keywords: Autosomal dominant disease; Familial benign chronic pemphigus; Hailey-Hailey disease.

Publication types

Case Reports