[Major beta-thalassemia and bone marrow allograft. Two cases and a study of the literature]

Pediatrie. 1987;42(8):637-44.
[Article in French]

Abstract

A 5 year 9 month-old boy has received a bone marrow allograft for beta-thalassaemia major. Conditioning included busulfan: 16 mg/kg, cyclophosphamide 200 mg/kg and a (6 Gy) thoracoabdominal irradiation. After a 16 months follow-up, the child is currently in complete remission without treatment with all the markers of his donor. His 9 year-old sister has been allografted for beta-thalassaemia major, with the same conditioning regimen. After engraftment, rejection occurred at day 85 with severe aplastic anaemia. A second graft was performed with the same donor without engraftment and the patient died at day 18 of pneumonitis. A review of the literature is proposed and the ethical choices are discussed.

Publication types

  • Case Reports
  • English Abstract
  • Review

MeSH terms

  • Bone Marrow Transplantation*
  • Busulfan / therapeutic use
  • Cyclophosphamide / therapeutic use
  • Humans
  • Infant
  • Male
  • Postoperative Complications
  • Thalassemia / therapy*
  • Thorax / radiation effects
  • Transplantation, Homologous

Substances

  • Cyclophosphamide
  • Busulfan