Primary pulmonary Ewing sarcoma/peripheral primitive neuroectodermal tumor

Aaron J Sohn; Benjamin Lang; Michael McCarroll; Atin Agarwal

doi:10.1080/08998280.2020.1798723

Primary pulmonary Ewing sarcoma/peripheral primitive neuroectodermal tumor

Proc (Bayl Univ Med Cent). 2020 Aug 19;33(4):646-648. doi: 10.1080/08998280.2020.1798723.

Authors

Aaron J Sohn¹, Benjamin Lang¹, Michael McCarroll², Atin Agarwal¹

Affiliations

¹ Department of Pathology, Baylor University Medical Center, Dallas, Texas.
² Department of Radiology, Baylor University Medical Center, Dallas, Texas.

Abstract

Ewing sarcoma/peripheral primitive neuroectodermal tumor (ES/pPNET) is a malignant small round cell sarcoma commonly occurring among children, adolescents, and adults. We report a rare case of ES/pPNET arising from the lung in a 49-year-old woman. She was found to have a mass in the right lung on a screening imaging study for her BRCA2 mutation. A lobectomy was performed and the mass had histological, immunohistochemical, and molecular features of ES/pPNET. Few cases of primary pulmonary Ewing sarcoma have been reported.

Keywords: Ewing sarcoma; peripheral primitive neuroectodermal tumor; primary lung tumor.

Publication types

Case Reports