Clinical presentation of a neuropsychiatric lupus patient with symmetrical basal ganglia lesions containing cytotoxic oedema cores surrounded by vasogenic oedema

Mod Rheumatol Case Rep. 2020 Jan;4(1):39-46. doi: 10.1080/24725625.2019.1651955. Epub 2019 Aug 20.

Abstract

Neuropsychiatric (NP) manifestations of systemic lupus erythematosus (SLE) are diverse, but involvement of basal ganglia is rare. We describe here a 28-year-old woman with NPSLE presenting aseptic meningitis accompanied by elevated interleukin-6 levels in the cerebrospinal fluid, who developed symmetrical basal ganglia lesions, containing a cytotoxic oedematous core, surrounded by vasogenic oedema upon magnetic resonance imaging. We were able to observe these lesions from a de novo appearance during the disease onset to its disappearance during immunosuppressive treatment. Reversibility upon immunosuppressive treatment indicated that autoimmune mediated mechanisms could contribute to the basal ganglia lesions in NPSLE.

Keywords: Systemic lupus erythematosus (SLE); basal ganglia; cytotoxic oedema; neuropsychiatric SLE (NPSLE); vasogenic oedema.

Publication types

  • Case Reports

MeSH terms

  • Adult
  • Basal Ganglia / drug effects
  • Basal Ganglia / pathology*
  • Edema / diagnosis*
  • Edema / drug therapy
  • Edema / etiology*
  • Female
  • Humans
  • Immunosuppressive Agents / pharmacology
  • Immunosuppressive Agents / therapeutic use
  • Lupus Erythematosus, Systemic / complications
  • Lupus Erythematosus, Systemic / diagnosis
  • Lupus Erythematosus, Systemic / drug therapy
  • Lupus Vasculitis, Central Nervous System / diagnosis*
  • Lupus Vasculitis, Central Nervous System / drug therapy
  • Lupus Vasculitis, Central Nervous System / etiology
  • Symptom Assessment

Substances

  • Immunosuppressive Agents