Anterior mediastinal neurofibrosarcoma-a rare manifestation of neurofibromatosis type-1

Indian J Thorac Cardiovasc Surg. 2018 Oct;34(4):510-512. doi: 10.1007/s12055-018-0673-8. Epub 2018 Apr 5.

Abstract

Anterior mediastinal neurofibroma and neurofibrosarcoma form a rare class of tumors seen in patients of neurofibromatosis. We describe a case of anterior mediastinal neurofibrosarcoma in a known case of neurofibromatosis type-1.

Keywords: Breathlessness; Neurofibromatosis; Neurofibrosarcoma.