Anterior mediastinal neurofibroma and neurofibrosarcoma form a rare class of tumors seen in patients of neurofibromatosis. We describe a case of anterior mediastinal neurofibrosarcoma in a known case of neurofibromatosis type-1.
Keywords: Breathlessness; Neurofibromatosis; Neurofibrosarcoma.
© Indian Association of Cardiovascular-Thoracic Surgeons 2018.