Atypical teratoid rhabdoid tumor (AT/RT) at the cerebellopontine angle arising from acoustic nerve with facial nerve palsy: report of a case

Abstract

Atypical teratoid rhabdoid tumor (AT/RT) is a highly aggressive central nervous system embryonic tumor predominantly occurring in infants and young children. The AT/RT can occur in the cerebellopontine angle and cause facial nerve palsy as a presenting sign. We present a case of a 2-year-old girl with a cerebellopontine angle tumor who initially presented with acute facial palsy. Later, asubsequent diagnosis of AT/RT was made.

Keywords: Atypical teratoid rhabdoid tumor; acoustic nerve; cerebellopontine angle; facial nerve palsy.