Dyke-Davidoff-Masson syndrome presenting as recurrent chronic headache in the late adult life

Wafa Ali Aldhaleei; Akshaya Srikanth Bhagavathula; Fatema Alshehhi

doi:10.4103/bc.bc_45_19

Dyke-Davidoff-Masson syndrome presenting as recurrent chronic headache in the late adult life

Brain Circ. 2020 Jun 26;6(2):123-125. doi: 10.4103/bc.bc_45_19. eCollection 2020 Apr-Jun.

Authors

Wafa Ali Aldhaleei¹, Akshaya Srikanth Bhagavathula², Fatema Alshehhi³

Affiliations

¹ Department of Gastroenterology, Sheikh Shakhbout Medical City (SSMC), Abu Dhabi, UAE.
² Department of Internal Medicine, UAE University, Al Ain, UAE.
³ Department of Internal Medicine, Sheikh Khalifa Medical City (SKMC), Abu Dhabi, UAE.

Abstract

Dyke-Davidoff-Masson syndrome (DDMS) (also referred to as cerebral hemiatrophy) is a rare condition characterized by seizures, facial asymmetry, contralateral spastic hemiplegia, or hemiparesis, with or without learning difficulties. It usually presents in the early childhood or late adolescence. The diagnosis is mainly associated with the presence of radiologic findings which include contralateral cerebral hemiatrophy with ipsilateral dilatation of the lateral ventricle and hypertrophy of the sinuses. Here, we report a case of a 49-year-old female patient who presented with chronic headache episodes for 10 years, and radiological findings revealed the DDMS.

Keywords: Cerebral hemiatrophy; Dyke–Davidoff–Masson syndrome; United Arab Emirates; radiology; seizures; severe headache.

Publication types

Case Reports