Amyopathic dermatomyositis with diffuse lung disease

Sumeera Bandi; Vidushi Jain; Ashish K Jaiswal

doi:10.4103/jfmpc.jfmpc_106_20

Amyopathic dermatomyositis with diffuse lung disease

J Family Med Prim Care. 2020 Jun 30;9(6):3147-3150. doi: 10.4103/jfmpc.jfmpc_106_20. eCollection 2020 Jun.

Authors

Sumeera Bandi¹, Vidushi Jain², Ashish K Jaiswal³

Affiliations

¹ Department of Pulmonary Medicine, HIMSR, Delhi, India.
² Department of Dermatology, Dermalinks, Ghaziabad, Uttar Pradesh, India.
³ Department of Pulmonary Medicine NIIMS, Greater Noida, Uttar Pradesh, India.

Abstract

A 38-year-old woman presented with progressively increasing breathlessness, recurrent productive cough, and intermittent fever of 1 year duration. Examination revealed cutaneous eruptions on the dorsal aspects of the hands and on face. Histopathologic features of skin biopsy revealed acanthosis, hyperkeratosis with focal vacuolar alteration of the basal-cell layer, and perivascular inflammatory infiltrates in upper dermis. CT scan showed diffuse lung disease and pulmonary function tests showed severe restrictive lung disease. There was no muscular involvement clinically or on electromyography and magnetic resonance imaging. She was diagnosed as a case of amyopathic dermatomyositis with diffuse lung disease and managed with topical and systemic steroid and topical sunscreen with fairly good response.

Keywords: Cutaneous lesions; dermatomyosiyis; lung disease.

Publication types

Case Reports