Arrhythmogenic Right Ventricular Cardiomyopathy: An Exuberant Case Affecting Both Ventricles

Circ Cardiovasc Imaging. 2020 Sep;13(9):e010243. doi: 10.1161/CIRCIMAGING.119.010243. Epub 2020 Sep 2.
No abstract available

Keywords: arrhythmogenic right ventricular cardiomyopathy; implantable defibrillators; magnetic resonance imaging; plakophilin 2; ventricular tachycardia.

Publication types

  • Case Reports
  • Video-Audio Media

MeSH terms

  • Amiodarone / administration & dosage
  • Anti-Arrhythmia Agents / administration & dosage
  • Arrhythmogenic Right Ventricular Dysplasia / complications*
  • Arrhythmogenic Right Ventricular Dysplasia / diagnosis
  • Arrhythmogenic Right Ventricular Dysplasia / physiopathology
  • Arrhythmogenic Right Ventricular Dysplasia / therapy
  • Bundle-Branch Block / diagnosis
  • Bundle-Branch Block / etiology*
  • Bundle-Branch Block / physiopathology
  • Bundle-Branch Block / therapy
  • Defibrillators, Implantable
  • Electric Countershock / instrumentation
  • Electrocardiography
  • Electrophysiologic Techniques, Cardiac
  • Heart Rate* / drug effects
  • Humans
  • Infusions, Intravenous
  • Male
  • Middle Aged
  • Secondary Prevention
  • Tachycardia, Ventricular / diagnosis
  • Tachycardia, Ventricular / etiology*
  • Tachycardia, Ventricular / physiopathology
  • Tachycardia, Ventricular / therapy
  • Treatment Outcome
  • Ventricular Function, Left*
  • Ventricular Function, Right*

Substances

  • Anti-Arrhythmia Agents
  • Amiodarone