[Sclerosing pneumocytoma: A rare and benign tumor]

Rev Mal Respir. 2020 Nov;37(9):743-747. doi: 10.1016/j.rmr.2020.08.003. Epub 2020 Aug 28.
[Article in French]

Abstract

Introduction: Sclerosing pneumocytoma is a benign and rare lung tumor affecting epithelial cells. In most cases, patients are asymptomatic and the diagnosis is made on an X ray or a CT scan performed for other enquiry. Sex ratio favors women. Epidemiological studies report that middle-aged Asian women are more frequently affected. Radiological investigations find a solitary nodule or a mass with peripheric localization. When performed, histological analysis shows a tumor composed of at least two of the four following architectures: papillary, sclerosing, hemangiomatous and solid, with two types of cells that can be round or cubic cells.

Cases report: We report two cases of multiple sclerosing pneumocytoma in two caucasien men. The first patient was asymptomatic, the second complain from moderate dyspnea. A wedge resection was performed in both, allowing diagnosis. Anatomopathology revealed respectively a predominant sclerosing and solid architecture and a sclerosing and papillary architecture. There was no progression of the other concomitant nodules after three years follow-up.

Conclusion: Pneumocytoma is a benign, slow-growing tumor with good prognosis.

Keywords: Benign tumor; Hémangiome sclérosant; Lung nodules; Nodules pulmonaires; Pneumocytome sclérosant; Rare tumor; Sclerosing hemangioma; Sclerosing pneumocytoma; Tumeur bénigne; Tumeur rare.

Publication types

  • Case Reports

MeSH terms

  • Disease Progression
  • Humans
  • Lung Neoplasms / diagnosis
  • Lung Neoplasms / pathology*
  • Lung Neoplasms / surgery*
  • Male
  • Middle Aged
  • Neoplasm Staging
  • Pneumonectomy
  • Prognosis
  • Pulmonary Sclerosing Hemangioma / diagnosis
  • Pulmonary Sclerosing Hemangioma / pathology*
  • Pulmonary Sclerosing Hemangioma / surgery*
  • Radiography, Thoracic
  • Rare Diseases