Superior-inferior ventricular arrangement with double-outlet left ventricle and malposition of the great arteries is an extremely rare congenital cardiac anomaly. The authors present the case of an infant who presented with cyanosis and respiratory distress. To the best of our knowledge, this is the first case reported.
Keywords: congenital heart disease; double outlet left ventricle; subpulmonary conus; superior-inferior cardiac ventricles.