In 1977, Carney et al. first described an association of gastric epithelioid leiomyosarcoma or gastrointestinal stromal tumor (GIST), pulmonary chondroma, and extra-adrenal paraganglioma. This previously unrecognized disorder came to be known as Carney's triad. We describe a case of a 27-year-old female with metastatic GIST, diagnosed with Carney's triad following pulmonary wedge resection, and highlight the surgical implication of this rare disease association.
Keywords: benign or congenital lesions; cancer; chest; genetic syndromes; lung; metastases/metastasectomy.
Copyright © 2020, Benissan-Messan et al.