Relapsed Wilms' tumor in pediatric patients: challenges in low- to middle-income countries-a single-center experience

J Egypt Natl Canc Inst. 2020 May 1;32(1):21. doi: 10.1186/s43046-020-00032-6.

Abstract

Background: Wilms' tumor (WT) affects one in 10,000 children and accounts for 5% of all childhood cancers. Although the overall relapse rate for children with WT has decreased to less than 15 %, the overall survival for patients with recurrent disease remains poor at approximately 50 %. The aim of the study to evaluate the outcome of relapsed Wilms' tumor pediatric patients treated at the National Cancer Institute (NCI), Egypt, between January 2008 and December 2015.

Results: One hundred thirty (130) patients diagnosed with WT during the study period, thirty (23%) patients had relapsed. The median follow up period was 22.3 months (range 3.6-140 months). The Overall Survival (OS) was 30.9% while the event-free survival (EFS) was 29.8% at a 5-year follow up period. Median time from diagnosis to relapse was 14.4 months. A second complete remission was attained in 18/30 patients (60%). The outcome of the 30 patients; 11 are alive and 19 had died. Three factors in our univariate analysis were prognostically significant for survival after relapse. The first was radiotherapy given after relapse (p = 0.012). The 5-year EFS and OS for the group that received radiotherapy were 41.9% versus 16.7% and 11.1% respectively for those that did not. The second was the state of lymph nodes among patients with local stage III (p = 0.004). Lastly, when risk stratification has been applied retrospectively on our study group, it proved to be statistically significant (p = 0.029).

Conclusion: Among relapsed pediatric WT, radiotherapy improved survival at the time of relapse and local stage III with positive lymph nodes had the worst survival among other stage III patients.

Keywords: Post-relapse survival; Radiotherapy; Relapse; Risk stratification; Wilms’ Tumor.

MeSH terms

  • Antineoplastic Combined Chemotherapy Protocols / economics
  • Antineoplastic Combined Chemotherapy Protocols / therapeutic use*
  • Chemoradiotherapy, Adjuvant / economics
  • Chemoradiotherapy, Adjuvant / methods
  • Chemoradiotherapy, Adjuvant / statistics & numerical data
  • Child, Preschool
  • Developing Countries
  • Disease-Free Survival
  • Egypt / epidemiology
  • Feasibility Studies
  • Female
  • Follow-Up Studies
  • Humans
  • Kidney Neoplasms / diagnosis
  • Kidney Neoplasms / economics
  • Kidney Neoplasms / mortality
  • Kidney Neoplasms / therapy*
  • Male
  • Neoplasm Recurrence, Local / diagnosis
  • Neoplasm Recurrence, Local / economics
  • Neoplasm Recurrence, Local / mortality
  • Neoplasm Recurrence, Local / therapy*
  • Nephrectomy / economics
  • Nephrectomy / methods*
  • Prognosis
  • Retrospective Studies
  • Wilms Tumor / diagnosis
  • Wilms Tumor / economics
  • Wilms Tumor / mortality
  • Wilms Tumor / therapy*