It is not asthma! An arcane case of 'Scimitar' syndrome: A case report

Med J Malaysia. 2020 Mar;75(2):184-185.

Abstract

'Scimitar' syndrome in adulthood is usually asymptomatic. Significant structural abnormalities symptoms usually manifest early during infancy or young childhood with features of congestive heart failure from significant shunting of the anomalous pulmonary venous drainage. Diagnosis of 'Scimitar' Syndrome in adults is rare and usually an incidental finding on chest radiograph. Here, we report a case of an adult who presented with symptoms in her 40's. This syndrome has never been reported nor discussed in Malaysia. This is the first case report of 'Scimitar' Syndrome in Malaysian literature. The diagnostic dilemma, medical management, and multi-disciplinary management by cardiology, physiotherapy and pulmonary rehabilitation teams are discussed.

Publication types

  • Case Reports

MeSH terms

  • Adult
  • Asthma / diagnosis*
  • Diagnosis, Differential
  • Female
  • Humans
  • Malaysia
  • Scimitar Syndrome / diagnosis*
  • Scimitar Syndrome / physiopathology