A Rare Case of Isolated Unilateral Atresia of Pulmonary Artery in an Elderly Female

Qurat Ul Ain; Omair A Khan; Mahnoor Sherazi; Mirza Faris Ali Baig; Fakeha Siddiqui

doi:10.7759/cureus.5869

A Rare Case of Isolated Unilateral Atresia of Pulmonary Artery in an Elderly Female

Cureus. 2019 Oct 9;11(10):e5869. doi: 10.7759/cureus.5869.

Authors

Qurat Ul Ain¹, Omair A Khan², Mahnoor Sherazi², Mirza Faris Ali Baig³, Fakeha Siddiqui⁴

Affiliations

¹ Internal Medicine, Medstar Health, Baltimore, USA.
² Internal Medicine, Fauji Foundation Hospital, Rawalpindi, PAK.
³ Internal Medicine, University of Pittsburgh Medical Center McKeesport, Pittsburgh, USA.
⁴ Internal Medicine, Dow University of Health Sciences, Karachi, PAK.

Abstract

Isolated unilateral agenesis/atresia of pulmonary artery (IUAPA) is a rare congenital disorder, an uncommon variant of unilateral agenesis of pulmonary artery (UAPA). Patients with IUAPA may remain asymptomatic and undiagnosed till late adulthood as they present with vague symptoms which may be overlooked. We report a case of IUAPA of right pulmonary artery in an elderly female who presented with complaints of productive cough and exertional dyspnea. Due to the formation of extensive collaterals, her lung parenchyma was preserved.

Keywords: cardiothoracic; congenital disorder; isolated atresia of pulmonary artery.

Publication types

Case Reports