Fetal umbilical-systemic shunt with a positive issue

J Gynecol Obstet Hum Reprod. 2020 Apr;49(4):101656. doi: 10.1016/j.jogoh.2019.101656. Epub 2019 Nov 21.

Abstract

We herein report the case of abnormal umbilical-venous return in which the antenatal ultrasound enabled us to establish the diagnosis of umbilical-systemic shunt (Type 1 according to Achiron (Achiron and Kivilevitch, 2016)). Due to the concomitant associations of cardiomegaly, intrauterine growth retardation, oligohydramnios, and left-lobe hypoplasia with agenesis of the intrahepatic umbilical vein - left portal vein - ductus venosus, a poor prognosis (11.1% survival) was to be expected. In spite of development of pulmonary arterial hypertension at birth, which was promptly treated, the evolution was nevertheless good, both on clinical and ultrasound follow-up.

Keywords: Agenesis ductus venosus; Fetal umbilical-portal-systemic venous shunts; Postnatal outcome.

Publication types

  • Case Reports

MeSH terms

  • Adult
  • Cesarean Section
  • Ductus Arteriosus, Patent / diagnostic imaging
  • Female
  • Fetal Growth Retardation / diagnostic imaging
  • Gestational Age
  • Humans
  • Infant, Newborn
  • Male
  • Oligohydramnios
  • Portal Vein / abnormalities
  • Pregnancy
  • Pregnancy Outcome
  • Ultrasonography, Prenatal*
  • Umbilical Veins / abnormalities*
  • Umbilical Veins / diagnostic imaging*
  • Ventricular Function, Left