Aortopulmonary Window With Pulmonary Atresia and Interrupted Aortic Arch: A Very Rare Triad

World J Pediatr Congenit Heart Surg. 2019 Nov;10(6):791-792. doi: 10.1177/2150135119872199.

Abstract

Aortopulmonary window (APW) is a rare lesion, accounting for 0.2% to 0.6% of all congenital heart diseases. We report a rare case of an infant with APW, interrupted aortic arch, and pulmonary atresia with intact interventricular septum and right ventricle-dependent coronary circulation. This report describes the anatomy of this lesion set, the complex surgical palliation that was required, and the management of postoperative complications.

Publication types

  • Case Reports

MeSH terms

  • Abnormalities, Multiple*
  • Aorta, Thoracic / abnormalities*
  • Aorta, Thoracic / diagnostic imaging
  • Aorta, Thoracic / surgery
  • Aortopulmonary Septal Defect / diagnosis
  • Aortopulmonary Septal Defect / surgery*
  • Cardiac Surgical Procedures / methods*
  • Computed Tomography Angiography
  • Humans
  • Imaging, Three-Dimensional
  • Infant, Newborn
  • Male
  • Pulmonary Artery / abnormalities
  • Pulmonary Artery / diagnostic imaging
  • Pulmonary Artery / surgery*
  • Pulmonary Atresia / diagnosis
  • Pulmonary Atresia / surgery*