[Tumor-induced osteomalacia caused by nasal hemangiopericytoma: a case report]

Zhonghua Er Bi Yan Hou Tou Jing Wai Ke Za Zhi. 2019 Aug 7;54(8):615-617. doi: 10.3760/cma.j.issn.1673-0860.2019.08.012.
[Article in Chinese]

Abstract

该例患者初期以全身骨痛为主要表现,其后出现间断鼻出血,最终病理确诊为鼻腔血管外皮瘤导致的肿瘤诱导性骨软化症。通过手术切除鼻腔肿瘤,患者病症解除。肿瘤诱导性骨软化症是一种罕见的副肿瘤综合征,通常表现为骨痛、骨折、肌肉无力,肿瘤主要通过分泌成纤维细胞生长因子23影响肾脏对磷的重吸收,导致低血磷性骨质软化症。鼻腔肿瘤以全身症状为首发表现的情况罕见,需引起耳鼻咽喉头颈外科医生的重视。.

Publication types

  • Case Reports

MeSH terms

  • Hemangiopericytoma / complications*
  • Hemangiopericytoma / surgery
  • Humans
  • Neoplasms, Connective Tissue / etiology*
  • Neoplasms, Connective Tissue / surgery
  • Nose Neoplasms / complications*
  • Nose Neoplasms / surgery
  • Osteomalacia
  • Paraneoplastic Syndromes / etiology*
  • Paraneoplastic Syndromes / surgery

Supplementary concepts

  • Oncogenic osteomalacia