Successful orthotopic heart transplantation in a patient with Marfan syndrome

J Card Surg. 2019 Sep;34(9):875-876. doi: 10.1111/jocs.14129. Epub 2019 Jun 24.

Abstract

Cardiovascular diseases represent the leading cause of mortality in patients with Marfan syndrome. Many treatments have been developed for patients with end-stage heart failure, among which orthotopic heart transplantation remains the gold standard. We report a successful orthotopic heart transplantation for a Marfan syndrome patient in end-stage heart failure.

Keywords: Marfan syndrome; cardiovascular complication; heart transplantation.

Publication types

  • Case Reports

MeSH terms

  • Adult
  • Female
  • Heart Failure / etiology
  • Heart Failure / physiopathology
  • Heart Failure / surgery*
  • Heart Transplantation / methods*
  • Humans
  • Marfan Syndrome / complications
  • Marfan Syndrome / diagnosis
  • Marfan Syndrome / surgery*
  • Tomography, X-Ray Computed
  • Treatment Outcome
  • Ventricular Function, Right / physiology