Fibrosarcoma of the ethmoid sinus: A rare entity

Najib Zouhair; Anass Chaouki; Amine Ballage; Redalah Elarabi Abada; Sami Rouadi; Mohamed Roubal; Mohamed Mahtar

doi:10.1016/j.ijscr.2019.05.023

Fibrosarcoma of the ethmoid sinus: A rare entity

Int J Surg Case Rep. 2019:59:136-139. doi: 10.1016/j.ijscr.2019.05.023. Epub 2019 May 14.

Authors

Najib Zouhair¹, Anass Chaouki², Amine Ballage², Redalah Elarabi Abada², Sami Rouadi², Mohamed Roubal², Mohamed Mahtar²

Affiliations

¹ Department of Otorhinolaryngology, Hospital of 20 August, University of Hassan II, Casablanca, Morocco. Electronic address: najib_zouhair@hotmail.fr.
² Department of Otorhinolaryngology, Hospital of 20 August, University of Hassan II, Casablanca, Morocco.

Abstract

Introduction: Ethmoidal fibrosarcoma is an extremely rare tumor which represent less than one percent of all malignancies in this anatomical area, the case of a 13-year-old is reported here.

Presentation of case: A 13-year-old boy, his medical history was marked exclusively before presented to our hospital by an exophthalmia. Rhinoscopic examination showed well-defined pink mass at the level of ethmoid. Computed tomography was performed to showed local and regional extension. Treatment was an endoscopic excision of the tumor using a navigation system. The final diagnosis was made on pathologic examination. Radiotherapy was recommended by multidisciplinary staff but the patient refused.

Discussion: These tumors occur in extremities most frequently and Ethmoidal localization is extremely rare and have no specifics symptoms, so the rhinoscopic examination is necessary for any chronic nasal symptom. Its treatment is not codified because of its rarity and its prognosis is unknown.

Conclusion: It's important knowledge about this pathology because of its rarity and its therapeutic and prognostic difficulties.

Keywords: Endoscopy; Ethmoid; Fibrosarcoma; Histopathology; Navigation.