Cystic fibrosis year in review 2018, part 2

Pediatr Pulmonol. 2019 Aug;54(8):1129-1140. doi: 10.1002/ppul.24365. Epub 2019 May 24.

Abstract

Cystic fibrosis (CF) research and case reports were robust in the year 2018. This report summarizes publications related the multisystem effects of CF, pulmonary exacerbations, new and expanded therapies other than cystic fibrosis transmembrane conductance regulator modulator studies, and patient-reported priorities and outcomes.

Keywords: cystic fibrosis (CF); depression; nutrition; pulmonary exacerbation.

Publication types

  • Review

MeSH terms

  • Cystic Fibrosis* / complications
  • Cystic Fibrosis* / drug therapy
  • Cystic Fibrosis* / physiopathology
  • Humans
  • Lung / physiopathology
  • Patient Reported Outcome Measures