Type II Abernethy Malformation in a Patient with Primary Budd-Chiari Syndrome

Ann Hepatol. 2019 Jan-Feb;18(1):246-249. doi: 10.5604/01.3001.0012.7933.

Abstract

Budd-Chiari syndrome (BCS) is a heterogeneous group of disorders characterized by hepatic venous outflow obstruction. Abernethy malformation is a congenital vascular malformation defined by diversion of portal blood away from the liver. Both conditions are rare vascular diseases. We report here the first case of a patient with combined type II Abernethy malformation and BCS from China. The inferior vena cava obstruction was treated with percutaneous balloon angioplasty; close follow-up was elected for the Abernethy malformation.

Keywords: Angiography; Congenital porto-systemic shunt; Hepatic venous outflow obstruction; Inferior vena cava.

Publication types

  • Case Reports

MeSH terms

  • Angiography, Digital Subtraction
  • Angioplasty, Balloon / methods*
  • Budd-Chiari Syndrome / diagnosis*
  • Budd-Chiari Syndrome / surgery
  • Computed Tomography Angiography
  • Diagnosis, Differential
  • Female
  • Humans
  • Middle Aged
  • Portal Vein / abnormalities*
  • Portal Vein / surgery
  • Ultrasonography, Doppler, Duplex
  • Vascular Malformations / diagnosis*
  • Vascular Malformations / surgery
  • Vena Cava, Inferior / diagnostic imaging
  • Vena Cava, Inferior / surgery*

Supplementary concepts

  • Patent Ductus Venosus