Cystic fibrosis year in review 2018, part 1

Pediatr Pulmonol. 2019 Aug;54(8):1117-1128. doi: 10.1002/ppul.24361. Epub 2019 May 20.

Abstract

Cystic fibrosis research and case reports were robust in the year 2018. This report summarizes research and cases related to Cystic Fibrosis Transmembrane Conductance Regulator (CFTR) modulator therapies, inflammation and infection, epidemiology and the physiologic, and imaging assessment of disease.

Keywords: antibiotic therapy; clinical trials; cystic fibrosis (CF); epidemiology; pulmonary function testing (PFT).

Publication types

  • Review

MeSH terms

  • Cystic Fibrosis Transmembrane Conductance Regulator*
  • Cystic Fibrosis* / drug therapy
  • Cystic Fibrosis* / epidemiology
  • Cystic Fibrosis* / microbiology
  • Cystic Fibrosis* / physiopathology
  • Humans
  • Infections / diagnosis
  • Infections / epidemiology

Substances

  • CFTR protein, human
  • Cystic Fibrosis Transmembrane Conductance Regulator