Background: Propriospinal myoclonus is an infrequent type of hyperkinetic movement that can be commonly idiopathic but also may occur after spinal cord lesions.
Phenomenology shown: We describe an 8-year-old female showing repetitive flexor and extensor arrhythmic brief jerks of the trunk, compatible with propriospinal myoclonus secondary to cervical myelopathy.
Educational value: Isolated propriospinal myoclonus may be the clinical sign that leads to the diagnosis of incipient myelopathy.
Keywords: Arnold–Chiari; Clinical neurology examination; myoclonus; propriospinal myoclonus; sickle-cell disease; spinal cord.