The trileaflet mitral valve is a very rare congenital malformation with three equal size leaflets and three papillary muscles. In this article, we report the first case of trileaflet mitral valve associated with a bicuspid aortic valve in a patient referred for management of infective endocarditis. <Learning objective: A trileaflet mitral valve is a rare congenital anomaly. There are two cases described in the literature, one associated with hypertrophic cardiomyopathy and the other with a subvalvular stenosis. To the best of our knowledge, we believe that this is the first description of trileaflet mitral valve associated with bicuspid aortic valve.>.
Keywords: Congenital malformation; Echocardiography; Trileaflet mitral valve.