Infantile Cortical Hyperostosis

Excerpt

Infantile cortical hyperostosis (ICH), also known as Caffey disease, was first reported by Roske in 1930 and described by Caffey and Silverman in 1945. ICH is a disorder affecting the skeletal system of infants. ICH most commonly affects the mandible (70% to 90% of cases) and has the appearance of a periosteal reaction. ICH is also known to affect the clavicle, rib, ulna, scapula, and rarely the ilia, parietal bones, and metatarsals. Usually unilateral when involving the scapula. Primary bone lesions are commonly asymmetric and localized to the diaphysis with sparing of the metaphysis and epiphysis. This pattern of involvement usually results in spindle-shaped bones. The disease usually spontaneously resolves within 2 years.