[A case of mucoviscidosis in practical work of a pulmonologist]

Klin Med (Mosk). 2016;94(8):628-30.
[Article in Russian]

Abstract

A case of late manifestation ofmucoviscidosis is reported. In the past, this pathology was dealt with by pediatricians, but to-day the management of this problem involves a number of different specialists. The progress in clinical practice makes it possible to significantly prolong the life span of patients with this condition. The present case shows that its clinical manifestations may appear at any age.

Publication types

  • Case Reports

MeSH terms

  • Adult
  • Cystic Fibrosis Transmembrane Conductance Regulator / genetics
  • Cystic Fibrosis* / diagnosis
  • Cystic Fibrosis* / genetics
  • Cystic Fibrosis* / physiopathology
  • Cystic Fibrosis* / therapy
  • Humans
  • Lung* / diagnostic imaging
  • Lung* / microbiology
  • Lung* / physiopathology
  • Male
  • Patient Care Management / methods*
  • Respiratory Function Tests / methods
  • Tomography, Spiral Computed / methods
  • Treatment Outcome

Substances

  • Cystic Fibrosis Transmembrane Conductance Regulator