Right Heart-Pulmonary Circulation Unit in Cardiomyopathies and Storage Diseases

Heart Fail Clin. 2018 Jul;14(3):311-326. doi: 10.1016/j.hfc.2018.03.001.

Abstract

Cardiomyopathies (CM) are a heterogeneous group of muscle heart diseases, divided into 3 main categories (dilated, hypertrophic, and restrictive). In addition to these subgroups, athlete's heart and hypertensive cardiopathy are both the result of heart adaptation to increased loading conditions, making it possible to include them in the CM group. Right heart involvement is clear in some CM as arrhythmogenic CM, carcinoid syndrome, and endomyocardial fibrosis, whereas in others, like hypertrophic or dilated CM, it is known that the right heart has a prognostic impact but less clear is its pathogenic role.

Keywords: Athlete’s heart; Cardiac magnetic resonance; Dilated cardiomyopathies; Echocardiography; Hypertrophic cardiomyopathies; Restrictive cardiomyopathies; Right ventricle; Speckle tracking echocardiography.

Publication types

  • Review

MeSH terms

  • Cardiomegaly, Exercise-Induced / physiology
  • Cardiomyopathies / diagnostic imaging
  • Cardiomyopathies / physiopathology*
  • Heart Ventricles / diagnostic imaging
  • Heart Ventricles / physiopathology*
  • Humans
  • Pulmonary Circulation / physiology*
  • Ventricular Dysfunction, Right / diagnostic imaging
  • Ventricular Dysfunction, Right / physiopathology*