[Genetic analysis of two children patients affected with CHARGE syndrome]

Zhonghua Yi Xue Yi Chuan Xue Za Zhi. 2018 Apr 10;35(2):244-247. doi: 10.3760/cma.j.issn.1003-9406.2018.02.022.
[Article in Chinese]

Abstract

Objective: To analyze two Chinese pediatric patients with multiple malformations and growth and development delay.

Methods: Both patients were subjected to targeted gene sequencing, and the results were analyzed with Ingenuity Variant Analysis software. Suspected pathogenic variations were verified by Sanger sequencing.

Results: High-throughput sequencing showed that both patients have carried heterozygous variants of the CHD7 gene. Patient 1 carried a nonsense mutation in exon 36 (c.7957C>T, p.Arg2653*), while patient 2 carried a nonsense mutation of exon 2 (c.718C>T, p.Gln240*). Sanger sequencing confirmed the above mutations in both patients, while their parents were of wild-type for the corresponding sites, indicating that the two mutations have happened de novo.

Conclusion: Two patients were diagnosed with CHARGE syndrome by high-throughput sequencing.

Publication types

  • Case Reports

MeSH terms

  • CHARGE Syndrome / genetics*
  • DNA Helicases / genetics*
  • DNA-Binding Proteins / genetics*
  • Genetic Testing*
  • High-Throughput Nucleotide Sequencing
  • Humans
  • Infant
  • Male
  • Mutation*

Substances

  • DNA-Binding Proteins
  • DNA Helicases
  • CHD7 protein, human