A case report of congenital scoliosis associated with situs inversus totalis

Medicine (Baltimore). 2017 Dec;96(50):e9239. doi: 10.1097/MD.0000000000009239.

Abstract

Rationale: Situs inversus totalis is a rare anomaly disease in which the organs in the chest and abdomen are positioned in a mirror image reversal of normal positions. Although this has been confirmed to be associated with spinal abnormalities, reports about situs inversus totalis with congenital scoliosis remain limited.

Patient concerns: We present a 9-year-old girl having congenital scoliosis associated with situs inversus totalis.

Diagnoses: She also had other associated anomalies: ventricular septal defect, mild restrictive ventilatory dysfunction, hydronephrosis, and syringomyelia. Her preoperative Cobb angle (T11-L3) was 78°.

Interventions: She received single growing rods treatment and subsequent posterior spinal fusion correction surgery for her scoliosis.

Outcomes: The coronal Cobb angle of the main curve was corrected to 20° postoperatively and no obvious loss of spinal corrective angle was identified 1 year after the correction surgery.

Lessons: Growing rods technique could be a safe and effective alternative for the treatment of scoliosis associated with situs inversus totalis. In the correction of left-sided lumbar curve of this kind of patients, the risks of aorta impingements should not be neglected when placing pedicle screws on the concave sides.

Publication types

  • Case Reports

MeSH terms

  • Abnormalities, Multiple
  • Child
  • Female
  • Humans
  • Scoliosis / congenital*
  • Scoliosis / surgery*
  • Situs Inversus*