Endobronchial Lesion in Eosinophilic Granulomatosis with Polyangiitis

Iran J Allergy Asthma Immunol. 2017 Dec;16(6):561-564.

Abstract

Eosinophilic granulomatosis with polyangiitis is a systemic vasculitis. It could affect respiratory system, kidney, and central nervous system frequently; however, all body organs could be involved. Asthma and eosinophilic pneumonia are predominant manifestations in respiratory system. Bronchoalveolar lavage or lung biopsy may be used for diagnosis, but endobronchial lesion is not considered as a manifestation of eosinophilic granulomatosis with polyangiitis. Here we present a case of eosinophilic granulomatosis with polyangiitis with unusual endobronchial lesion which was confirmed by endobronchial biopsy.

Keywords: Bronchoscopy; Eosinophilic granulomatosis with polyangiitis; Vasculitis.

Publication types

  • Case Reports

MeSH terms

  • Biopsy
  • Bronchi / pathology*
  • Bronchoscopes
  • Eosinophils / pathology*
  • Granulomatosis with Polyangiitis / diagnosis*
  • Granulomatosis with Polyangiitis / drug therapy
  • Humans
  • Male
  • Methylprednisolone / therapeutic use
  • Middle Aged
  • Radiography, Thoracic
  • Respiratory Mucosa / pathology*
  • Tomography, X-Ray Computed
  • Treatment Outcome

Substances

  • Methylprednisolone