Non compaction cardiomyopathy: Review of a controversial entity

Abstract

Non-compaction cardiomyopathy is a heterogeneous and complex entity concerning which there are still many doubts to be resolved. While the American Heart Association includes it among genetic cardiomyopathies, the European Society of Cardiology treats it as an unclassified cardiomyopathy. It may present in a sporadic or familial form, isolated or associated with other heart diseases, affecting only the left ventricle or both and can sometimes appear as a mixed phenotype in patients with other cardiomyopathies. Different forms of clinical presentation are also associated with its different morphological manifestations, and even non-compaction of the left ventricle may be triggered by other physiological or pathological processes. The purpose of this review is an update of this entity and its controversies.

Keywords: Cardiomyopathy; Falta de compactación del ventrículo izquierdo; Left ventricle non-compaction; Miocardiopatía no compactada; Miocardiopatías; Non-compaction cardiomyopathy.