Mitochondrial Dysfunction in Pulmonary Fibrosis

Ann Am Thorac Soc. 2017 Nov;14(Supplement_5):S383-S388. doi: 10.1513/AnnalsATS.201705-370AW.

Abstract

The aging of the human population has resulted in an unprecedented increase in the incidence and prevalence of age-related diseases, including those of the lung. Idiopathic pulmonary fibrosis is a disease of aging, and is characterized by a progressive decline in lung function and high mortality. Recent studies suggest that mitochondrial dysfunction, which can accompany aging phenotypes, may contribute to the pathogenesis of idiopathic pulmonary fibrosis. In this review, we explore current evidence for mitochondrial dysfunction in alveolar epithelial cells, fibroblasts, and immune cells that participate in the fibrotic process. Further, the fates of these cell populations and the potential to target mitochondrial dysfunction as a therapeutic strategy are discussed.

Keywords: aging; mitochondrial dysfunction; pulmonary fibrosis.

Publication types

  • Review

MeSH terms

  • Aging / immunology
  • Aging / metabolism*
  • Alveolar Epithelial Cells / metabolism
  • Fibroblasts / metabolism
  • Humans
  • Idiopathic Pulmonary Fibrosis / immunology*
  • Idiopathic Pulmonary Fibrosis / metabolism*
  • Lung / physiopathology
  • Mitochondria / pathology*