Giant isolated transcranial Rosai-Dorfman disease with diffuse involvement of nasal and paranasal tissues: case report and literature review

Zhihong Zhong; Wei Fu; Yuhao Sun; Qingfang Sun; Liuguan Bian

doi:10.1080/02688697.2017.1344614

Giant isolated transcranial Rosai-Dorfman disease with diffuse involvement of nasal and paranasal tissues: case report and literature review

Br J Neurosurg. 2019 Jun;33(3):299-301. doi: 10.1080/02688697.2017.1344614. Epub 2017 Jul 3.

Authors

Zhihong Zhong¹, Wei Fu¹, Yuhao Sun¹, Qingfang Sun¹, Liuguan Bian¹

Affiliation

¹ a Department of Neurosurgery , Ruijin Hospital, Shanghai Jiao Tong University, School of Medicine , Shanghai , China.

PMID: 28670983
DOI: 10.1080/02688697.2017.1344614

Abstract

Rosai-Dorfman disease (RDD) is an uncommon systemic histioproliferative disease process characterized by sinus histiocytosis with massive lymphadenopathy, and isolated transcranial RDD (ITRDD) is extremely rare. We report a patient with giant ITRDD with diffuse involvement of nasal and paranasal tissues, showing favorable response to postoperative steroid therapy.

Keywords: Rosai-Dorfman disease; sinus histiocytosis; transcranial; treatment.

Publication types

Case Reports
Review
Video-Audio Media

MeSH terms

Anti-Inflammatory Agents / therapeutic use
Chemotherapy, Adjuvant
Cortisone / therapeutic use
Histiocytosis, Sinus / drug therapy
Histiocytosis, Sinus / pathology
Histiocytosis, Sinus / surgery*
Humans
Male
Middle Aged
Nose Diseases / drug therapy
Nose Diseases / pathology
Nose Diseases / surgery*
Paranasal Sinus Diseases / drug therapy
Paranasal Sinus Diseases / pathology
Paranasal Sinus Diseases / surgery
Postoperative Care / methods
Treatment Outcome

Substances

Anti-Inflammatory Agents
Cortisone