Haemodynamically proven pulmonary hypertension in a patient with GATA2 deficiency-associated pulmonary alveolar proteinosis and fibrosis
Eur Respir J
.
2017 May 11;49(5):1700407.
doi: 10.1183/13993003.00407-2017.
Print 2017 May.
Authors
Stéphane Jouneau
1
2
,
Alice Ballerie
2
3
,
Mallorie Kerjouan
4
,
Xavier Demant
5
,
Elodie Blanchard
5
,
Mathieu Lederlin
6
7
Affiliations
1
Dept of Respiratory Medicine, Pontchaillou Hospital, Rennes 1 University, Rennes, France Stephane.jouneau@chu-rennes.fr.
2
IRSET UMR1085, Rennes 1 University, Rennes, France.
3
Dept of Internal Medicine, Pontchaillou Hospital, Rennes 1 University, Rennes, France.
4
Dept of Respiratory Medicine, Pontchaillou Hospital, Rennes 1 University, Rennes, France.
5
Dept of Respiratory Medicine, Haut-Lévèque Hospital, Bordeaux University, Pessac, France.
6
Dept of Radiology, Pontchaillou Hospital, Rennes 1 University, Rennes, France.
7
LTSI, INSERM U1099, Rennes 1 University, Rennes, France.
PMID:
28495697
DOI:
10.1183/13993003.00407-2017
No abstract available
Publication types
Letter
Comment
MeSH terms
GATA2 Transcription Factor
Humans
Hypertension, Pulmonary*
Immunologic Deficiency Syndromes
Pulmonary Alveolar Proteinosis*
Substances
GATA2 Transcription Factor
GATA2 protein, human