[Cardiomyopathy and ion channel diseases registry: the Szeged CardioGen Registry]

Orv Hetil. 2017 Jan;158(3):101-105. doi: 10.1556/650.2017.30659.
[Article in Hungarian]

Abstract

The Szeged cardiomyopathy and ion channel diseases registry aims to establish a representative disease-specific registry based on the recruitment of patients with different cardiomyopathies and ion channel diseases followed at the Cardiology Center, University of Szeged. The registry collects patient data on the main forms of primary cardiomyopathies (hypertrophic, dilated, restrictive, arrhythmogenic right ventricular, left ventricular non-compact, tako-tsubo cardiomyopathy) and ion channel diseases (long QT syndrome, short QT syndrome, Brugada syndrome, catecholaminergic polymorphic ventricular tachycardia). Patients with hypertrophic cardiomyopathy (388 patients) make up the largest group of patients in the registry. Patients with dilated cardiomyopathy (310 patients) and patients with the long QT syndrome (111 patients) form two other sizable groups. Analyzed data of the group of patients with hypertrophic cardiomyopathy indicate similar figures with regard to disease related mortality and morbidity and clinical parameters. Orv. Hetil., 2017, 158(3), 101-105.

Keywords: cardiomyopathia; cardiomyopathy; ion channel diseases; ioncsatorna-betegség; prognosis; prognózis; registry; regiszter.

MeSH terms

  • Brugada Syndrome / diagnosis
  • Brugada Syndrome / epidemiology
  • Cardiology Service, Hospital
  • Cardiomyopathies / classification
  • Cardiomyopathies / diagnosis*
  • Cardiomyopathies / epidemiology*
  • Female
  • Humans
  • Ion Channel Gating / physiology*
  • Ion Channels
  • Male
  • Registries / statistics & numerical data*

Substances

  • Ion Channels