Cutaneous marginal zone lymphomas

Steven H Swerdlow

doi:10.1053/j.semdp.2016.11.007

Cutaneous marginal zone lymphomas

Semin Diagn Pathol. 2017 Jan;34(1):76-84. doi: 10.1053/j.semdp.2016.11.007. Epub 2016 Nov 29.

Author

Steven H Swerdlow¹

Affiliation

¹ Division of Hematopathology, Department of Pathology, University of Pittsburgh School of Medicine, UPMC-Presbyterian, G-335, 200 Lothrop Street, Pittsburgh, PA 15213. Electronic address: swerdlowsh@upmc.edu.

PMID: 27986434
DOI: 10.1053/j.semdp.2016.11.007

Abstract

Primary cutaneous marginal zone lymphoma (CMZL) is one of the major primary B-cell lymphomas of skin. Two types are recognized: a more common class-chain switched CMZL, and a much less common IgM+ CMZL. The extremely indolent course, together with other features distinct from most other MALT lymphomas, has led some to question whether at least the class-switched cases should be considered an overt lymphoma.

Keywords: B-cell lymphoma; IgG4; MALT lymphoma; Primary cutaneous marginal zone lymphoma; Skin.

Publication types

Review

MeSH terms

Humans
Lymphoma, B-Cell, Marginal Zone / diagnosis
Lymphoma, B-Cell, Marginal Zone / genetics
Lymphoma, B-Cell, Marginal Zone / pathology
Skin Neoplasms* / diagnosis
Skin Neoplasms* / genetics
Skin Neoplasms* / pathology