Why do some adults with PiMZ α1-antitrypsin develop bronchiectasis? [corrected]

ERJ Open Res. 2016 Jun 6;2(2):00021-2016. doi: 10.1183/23120541.00021-2016. eCollection 2016 Apr.

¹ Dept of Respiratory Medicine, University Children's Hospital, Hannover Medical School, Endstage and Obstructive Lung Disease Hannover (BREATH), Member of the German Center for Lung Research (DZL), Hannover, Germany.
² Molecular Genetics Unit, Instituto de Investigación de Enfermedades Raras (IIER), Instituto de Salud Carlos III (ISCIII), Madrid, Spain.
³ Dept of Pediatric Pneumology, Allergy and Neonatology, University Children's Hospital, Hannover Medical School, Endstage and Obstructive Lung Disease Hannover (BREATH), Member of the German Center for Lung Research (DZL), Hannover, Germany.

Abstract

Recurrent infections of the upper airways in early life may be a warning sign of inherited α₁-antitrypsin deficiency http://ow.ly/iJsF300kbyV.