Vigabatrin efficacy in GPR56-associated polymicrogyria: The role of GABAA receptor pathway

Epilepsia. 2016 Aug;57(8):1337-8. doi: 10.1111/epi.13453.
No abstract available

Publication types

  • Letter

MeSH terms

  • Child
  • Female
  • Follow-Up Studies
  • GABA Agents / therapeutic use*
  • Humans
  • Male
  • Polymicrogyria* / drug therapy
  • Polymicrogyria* / genetics
  • Polymicrogyria* / metabolism
  • Receptors, G-Protein-Coupled / genetics*
  • Receptors, GABA-A / metabolism*
  • Signal Transduction / drug effects
  • Signal Transduction / physiology*
  • Vigabatrin / therapeutic use*

Substances

  • ADGRG1 protein, human
  • GABA Agents
  • Receptors, G-Protein-Coupled
  • Receptors, GABA-A
  • Vigabatrin