Although a schwannoma can originate from any central or peripheral nerves, schwannomas originating from the nasal tip are extremely rare and only 4 cases have been reported so far in English literature. These 4 cases appeared solely without any other accompanying schwannomas. However, the authors recently treated a patient with a nasal tip schwannoma coexisting with vestibular schwannoma. The nasal tip schwannoma was successfully removed without cosmetic deformity by using an open rhinoplasty approach.