A single-center experience with undifferentiated embryonal sarcoma of the liver

Pediatr Blood Cancer. 2016 Dec;63(12):2246-2248. doi: 10.1002/pbc.26154. Epub 2016 Jul 18.

Abstract

Undifferentiated embryonal sarcoma of the liver (UESL) is a rare aggressive mesenchymal pediatric tumor. Previously, reported outcomes have been very poor. Here, we report a single-center experience of five patients with UESL treated with upfront gross total resection and adjuvant chemotherapy. We have a median follow-up of 8 years with a range from 5 to 19 years with 100% event-free survival.

Keywords: case series; sarcoma; undifferentiated embryonal sarcoma of the liver.

MeSH terms

  • Adolescent
  • Child
  • Child, Preschool
  • Female
  • Humans
  • Liver Neoplasms / therapy*
  • Male
  • Neoplasms, Germ Cell and Embryonal / therapy*
  • Sarcoma / therapy*