PNET of the kidney are rare, aggressive tumors that occur mainly in adolescents. The diagnosis of PNET is difficult, but is possible with pathognomonic radiological findings. Since a radical nephrectomy is generally not sufficient for PNET of the kidney, early diagnosis and treatment is essential for successful recovery.
Keywords: Muscle weakness; Neoplasia; Neoplasm metastasis; Nephrectomy; Neuroectodermal tumors.