An Extremely Rare Variant of Pulmonary Venous Atresia

Abstract

We describe an unusual case of a newborn with a rare variant of atresia of the common pulmonary vein that was mistaken for total anomalous pulmonary venous connection, cardiac type. The survival of patients with atresia of the common pulmonary vein is dependent on early diagnosis followed by immediate surgical repair, although early accurate diagnosis has been described as difficult in previous reports. Reverse aortic arch flow detected by echocardiography may be an important sign suggesting such a diagnosis.