IgG4-related systemic disease presenting with pleural effusion, ascites and dilated cardiomyopathy

Tumori. 2016 Nov 11;102(Suppl. 2). doi: 10.5301/tj.5000502.

Abstract

Purpose: We report the case of a patient with IgG4-related disease with multiple organ involvement, especially myocardium, that was successfully treated with prednisone.

Methods: We performed several serological tests, electrocardiogram, echocardiography, computed tomography and inguinal lymph node biopsy.

Results: We diagnosed the patient with IgG4-related disease by the elevated serum IgG4 level and histological lymph node findings.

Conclusions: This is the first reported case of IgG4-related disease with dilated cardiomyopathy.

Publication types

  • Case Reports

MeSH terms

  • Adult
  • Ascites / diagnosis
  • Ascites / drug therapy
  • Ascites / immunology*
  • Biopsy
  • Cardiomyopathy, Dilated / diagnosis*
  • Cardiomyopathy, Dilated / drug therapy
  • Cardiomyopathy, Dilated / immunology*
  • Electrocardiography
  • Humans
  • Immunoglobulin G / blood
  • Immunoglobulin G / immunology*
  • Lymph Nodes / pathology
  • Male
  • Pleural Effusion / diagnosis
  • Pleural Effusion / drug therapy
  • Pleural Effusion / immunology*
  • Prednisone / administration & dosage
  • Prednisone / therapeutic use
  • Radiography, Thoracic
  • Tomography, X-Ray Computed
  • Treatment Outcome

Substances

  • Immunoglobulin G
  • Prednisone