No abstract available
Keywords:
ACVRL1 gene mutation; Hereditary hemorrhagic telangiectasia; Pulmonary arterial hypertension; Sildenafil.
MeSH terms
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Activin Receptors, Type II / genetics
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Female
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Humans
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Hypertension, Pulmonary / drug therapy*
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Hypertension, Pulmonary / genetics
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Middle Aged
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Mutation, Missense
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Pedigree
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Pulmonary Arterial Hypertension
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Sildenafil Citrate / administration & dosage*
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Telangiectasis / congenital*
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Telangiectasis / drug therapy
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Telangiectasis / genetics
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Treatment Outcome
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Vasodilator Agents / administration & dosage
Substances
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Vasodilator Agents
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Sildenafil Citrate
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ACVRL1 protein, human
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Activin Receptors, Type II
Supplementary concepts
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Pulmonary Arterial Hypertension, Hereditary Hemorrhagic Telangiectasia-Related