Bilateral Neuroretinitis and a Unilateral Superior Hemivein Occlusion with Frosted Branch Angiitis Pattern Presenting Simultaneously in Behçet's Disease

Roy Schwartz; Sara Borok; Michaella Goldstein; Anat Kesler; Keren Regev; Ori Elkayam; Zohar Habot-Wilner

doi:10.1159/000444214

Bilateral Neuroretinitis and a Unilateral Superior Hemivein Occlusion with Frosted Branch Angiitis Pattern Presenting Simultaneously in Behçet's Disease

Case Rep Ophthalmol. 2016 Mar 9;7(1):141-7. doi: 10.1159/000444214. eCollection 2016 Jan-Apr.

Authors

Roy Schwartz¹, Sara Borok², Michaella Goldstein¹, Anat Kesler¹, Keren Regev³, Ori Elkayam², Zohar Habot-Wilner¹

Affiliations

¹ Ophthalmology Division, Tel Aviv Sourasky Medical Center, The Sackler Faculty of Medicine, Tel Aviv University, Tel Aviv, Israel.
² Rheumatology Unit, Tel Aviv Sourasky Medical Center, The Sackler Faculty of Medicine, Tel Aviv University, Tel Aviv, Israel.
³ Neurology Division, Tel Aviv Sourasky Medical Center, The Sackler Faculty of Medicine, Tel Aviv University, Tel Aviv, Israel.

Abstract

Purpose: To report a unique case of Behçet's disease that presented with atypical ocular manifestations.

Methods: Case report.

Results: A 23-year-old homosexual male presented with bilateral anterior uveitis, vitritis, neuroretinitis and a unilateral superior hemivein occlusion with frosted branch angiitis pattern. These were accompanied by systemic findings of recurrent oral aphthous ulcers, erythema nodosum, and neurological and gastrointestinal involvement. A positive HLA-B51 examination supported the diagnosis of Behçet's disease.

Conclusion: Neuroretinitis and frosted branch angiitis may be the clinical manifestations of Behçet's disease and may present simultaneously.

Keywords: Behçet's disease; Brain; Frosted branch angiitis; Gastrointestinal; Hemivein occlusion; Neuroretinitis; Ocular Behçet's disease; Panuveitis.

Publication types

Case Reports