Expanding the clinicopathological spectrum of late cutaneous Lyme borreliosis (acrodermatitis chronica atrophicans [ACA]): A prospective study of 20 culture- and/or polymerase chain reaction (PCR)-documented cases

J Am Acad Dermatol. 2016 Apr;74(4):685-92. doi: 10.1016/j.jaad.2015.10.046. Epub 2016 Jan 9.

Abstract

Background: The diagnosis of acrodermatitis chronica atrophicans (ACA), the late cutaneous manifestation of Lyme borreliosis, can be challenging. Histologic changes in ACA have been described in a few studies from endemic countries, relying on cases documented by serology only.

Objectives: We sought to reassess the clinicopathological spectrum of ACA in a series of thoroughly documented cases.

Methods: Patients prospectively included in a national prospective study were selected on the basis of positive culture and/or polymerase chain reaction of a skin biopsy sample. The diagnosis of ACA was confirmed by reviewing the clinical and serologic data. Histopathological samples were carefully reviewed.

Results: Twenty patients were included. Unusual clinical features (ie, numerous small violaceous patches and equidistant small spinous papules with background faint erythema) were observed in 2 patients. Histopathological examination revealed a classic plasma cell-rich perivascular and interstitial pattern with telangiectases in 16 of 25 samples, whereas strikingly prominent granuloma annulare-like or lichenoid features were observed in 4 and 2 of 25 cases, respectively, and discrete nonspecific minor changes in 3 of 25 cases.

Limitations: The small number of patients was a limitation.

Conclusions: Genuine culture- and/or polymerase chain reaction-proven ACA can rarely present as numerous violaceous patches or cluster of spinous papules clinically, and as a granuloma annulare-like or lichenoid dermatosis histologically.

Keywords: Borrelia burgdorferi; acrodermatitis chronica atrophicans; borreliosis; granuloma annulare; lichenoid dermatitis; plasma cells.

Publication types

  • Research Support, Non-U.S. Gov't

MeSH terms

  • Acrodermatitis / diagnosis*
  • Acrodermatitis / microbiology
  • Adult
  • Age Distribution
  • Aged
  • Aged, 80 and over
  • Biopsy, Needle
  • Borrelia burgdorferi / isolation & purification*
  • Cohort Studies
  • DNA, Bacterial / analysis
  • Erythema Chronicum Migrans / diagnosis*
  • Erythema Chronicum Migrans / epidemiology
  • Female
  • France / epidemiology
  • Humans
  • Immunohistochemistry
  • Incidence
  • Lyme Disease / diagnosis*
  • Lyme Disease / epidemiology
  • Male
  • Middle Aged
  • Polymerase Chain Reaction / methods*
  • Prognosis
  • Prospective Studies
  • Risk Assessment
  • Severity of Illness Index
  • Sex Distribution

Substances

  • DNA, Bacterial