Unilateral pulmonary artery atresia is a rare congenital defect. The affected lung in unilateral pulmonary artery atresia usually receives its blood supply from many collateral vessels including the coronary artery. We report a case of an elderly woman with suspected anginal symptoms who had a coronary artery fistula functioning as a collateral vessel due to unilateral pulmonary artery atresia.
Keywords: Pulmonary artery agenesis; collateral circulation; fractional flow reserve; myocardial ischaemia; myocardial perfusion imaging.